Mono­genic de­fects that cause β-cell dysfunc­tion, such as neona­tal di­a­betes and MODY, repre­sent a small frac­tion of pa­tients with di­a­betes (<5%). Table 2.7 de­scribes the most com­mon caus­es of mono­genic di­a­betes. For a com­pre­hen­sive list of caus­es, see Ge­net­ic Di­ag­no­sis of En­docrine Dis­or­ders (119).

Table 2.7 - Most com­mon caus­es of mono­genic di­a­betes (119)

AD, autosomal dominant; AR, autosomal recessive; IUGR, intrauterine growth restriction.